Massive Parallel DNA Sequencing of Patients with Inherited Cardiomyopathies in Cyprus and Suggestion of Digenic or Oligogenic Inheritance.
Constantina KoutsoftiMarios IoannidesChristiana PolydorouGregory PapagregoriouApostolos MalatrasGeorge MichaelIrene HadjiioannouStylianos PieriEleni M LoizidouChristos EftychiouElias PapasavvasTheodoros ChristophidesAnna AlkelaiManav KapoorAlan R ShuldinerPanayiotis AvraamidesConstantinos DeltasPublished in: Genes (2024)
Inherited cardiomyopathies represent a highly heterogeneous group of cardiac diseases. DNA variants in genes expressed in cardiomyocytes cause a diverse spectrum of cardiomyopathies, ultimately leading to heart failure, arrythmias, and sudden cardiac death. We applied massive parallel DNA sequencing using a 72-gene panel for studying inherited cardiomyopathies. We report on variants in 25 families, where pathogenicity was predicted by different computational approaches, databases, and an in-house filtering analysis. All variants were validated using Sanger sequencing. Familial segregation was tested when possible. We identified 41 different variants in 26 genes. Analytically, we identified fifteen variants previously reported in the Human Gene Mutation Database: twelve mentioned as disease-causing mutations (DM) and three as probable disease-causing mutations (DM?). Additionally, we identified 26 novel variants. We classified the forty-one variants as follows: twenty-eight (68.3%) as variants of uncertain significance, eight (19.5%) as likely pathogenic, and five (12.2%) as pathogenic. We genetically characterized families with a cardiac phenotype. The genetic heterogeneity and the multiplicity of candidate variants are making a definite molecular diagnosis challenging, especially when there is a suspicion of incomplete penetrance or digenic-oligogenic inheritance. This is the first systematic study of inherited cardiac conditions in Cyprus, enabling us to develop a genetic baseline and precision cardiology.
Keyphrases
- copy number
- mitochondrial dna
- genome wide
- heart failure
- left ventricular
- single molecule
- single cell
- circulating tumor
- dna methylation
- endothelial cells
- cell free
- escherichia coli
- type diabetes
- cystic fibrosis
- staphylococcus aureus
- cardiac surgery
- pseudomonas aeruginosa
- insulin resistance
- gene expression
- transcription factor
- atrial fibrillation
- data analysis
- acute kidney injury
- glycemic control