Myocardial disease and ventricular arrhythmia in Marfan syndrome: a prospective study.
Laura Muiño MosqueraHans De WildeDaniel DevosDanilo BabinLuc JordaensAnthony DemolderKatya De GrooteDaniel De WolfJulie De BackerPublished in: Orphanet journal of rare diseases (2020)
Our study shows mild but significant myocardial involvement in patients with MFS. Patients with previous surgery or valvular dysfunction are more severely affected. Evaluation of myocardial function with echocardiography and AECG should be considered in all patients with MFS, especially in those with valvular disease and a history of cardiac surgery.