Postoperative Morbidity and Interstage Hemodynamics Following Stage I Palliation in Patients with Turner Syndrome and Hypoplastic Left Heart Syndrome.
Sandra D KikanoSarah FuchsAndres Contreras VegaAnn Kavanaugh-McHughDavid P BichellStacy A S KillenPublished in: Pediatric cardiology (2023)
High mortality rates are described in TS + HLHS patients following S1P. In our cohort, despite most surviving more than 30 days post-S1P, long-term survival remained poor. Interstage catheterization data suggest poor physiologic candidacy for subsequent stages of single-ventricle palliation. Understanding the clinical and hemodynamic factors related to poor outcomes in TS + HLHS will help inform management for this population.
Keyphrases
- end stage renal disease
- ejection fraction
- newly diagnosed
- chronic kidney disease
- heart failure
- case report
- peritoneal dialysis
- electronic health record
- cardiovascular events
- pulmonary hypertension
- cardiovascular disease
- risk factors
- ultrasound guided
- coronary artery disease
- insulin resistance
- skeletal muscle
- left ventricular
- pulmonary arterial hypertension
- growth hormone
- glycemic control