Heart Transplantation for Ebstein Anomaly due to Late Surgical Presentation.
Tomas LengJoseph A DearaniElizabeth H StephensJonathan N JohnsonPublished in: World journal for pediatric & congenital heart surgery (2024)
Ebstein anomaly is a myopathy of the right ventricle characterized by failure of tricuspid valve delamination with accompanying tricuspid regurgitation. Its rarity, considerable anatomic variability, and frequent absence of symptoms can make the timing of surgery challenging. Contemporary tricuspid repair techniques can be performed with low mortality and bidirectional cavopulmonary anastomosis reduces the risk of operation when right ventricular function is poor. Here, we present a patient who presented late for surgery, failed high-risk conventional surgery and required heart transplantation.
Keyphrases
- aortic valve
- mitral valve
- minimally invasive
- coronary artery bypass
- aortic stenosis
- transcatheter aortic valve replacement
- surgical site infection
- case report
- left ventricular
- ejection fraction
- type diabetes
- heart failure
- cardiovascular disease
- coronary artery disease
- percutaneous coronary intervention
- cardiovascular events
- late onset
- risk factors
- early onset
- muscular dystrophy
- congenital heart disease