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Intranasal dexmedetomidine for adrenergic crisis in familial dysautonomia.

Christy L SpalinkErin BarnesJose Alberto PalmaLucy Norcliffe-KaufmannHoracio Kaufmann
Published in: Clinical autonomic research : official journal of the Clinical Autonomic Research Society (2017)
Intranasal dexmedetomidine is a feasible and safe acute treatment for adrenergic crisis in patients with familial dysautonomia. Further controlled studies are required to confirm the safety and efficacy in this population.
Keyphrases
  • public health
  • cardiac surgery
  • early onset
  • liver failure
  • respiratory failure
  • drug induced
  • acute kidney injury
  • intensive care unit
  • case control
  • extracorporeal membrane oxygenation
  • mechanical ventilation