Orbital mass and hairy kidney as characteristics of Erdheim-Chester disease.
Koichiro YamamotoKosuke OkaKou HasegawaFumio OtuskaPublished in: Clinical case reports (2021)
Erdheim-Chester disease (ECD) is a rare non-Langerhans cell histiocytosis, involving multiple organs. We report a case of ECD with typical features of an orbital mass and "hairy kidneys," whose recognition can lead to early diagnosis and treatment.