Towards an Imaging-centric Definition of Non-paraneoplastic Autoimmune Retinopathy.

Many eyes with npAIR exhibit a subacute, asymmetric generalized photoreceptor degeneration featuring outer retinal atrophy with relative foveal sparing, retinal vascular attenuation, absence of bone spicules, and speckled hypoautofluorescence often in a perimacular and perivenular distribution. Our findings augment diagnostic criteria to improve specificity and accessibility of testing for npAIR.