Biliary drainage as treatment for allograft steatosis following liver transplantation for PFIC-1 disease: A single-center experience.
Leina S AlrabadiRaffaella A MorottiPamela L ValentinoManuel I Rodriguez-DavalosUdeme D EkongSukru H EmrePublished in: Pediatric transplantation (2018)
Development of macrovesicular steatosis post-LT in patients with PFIC-1 is increasingly being observed, with the etiology not fully understood. We highlight successful and effective EBD for reversal of allograft steatosis in 2 patients with PFIC-1 disease and discuss our experience with internal biliary diversion in this patient population.