Pulmonary artery enlargement is associated with pulmonary hypertension and decreased survival in severe cystic fibrosis: A cohort study.

Aline N ZoukSwati GulatiDongqi XingKeith M WilleSteven M RoweJ Michael Wells

Published in: PloS one (2020)

PA enlargement is associated with pulmonary hemodynamics and PH in severe CF. PA enlargement is an independent prognostic indicator of PH and decreased survival in this population.

Keyphrases

pulmonary hypertension
pulmonary artery
cystic fibrosis
pulmonary arterial hypertension
coronary artery
early onset
pseudomonas aeruginosa
free survival
lung function