A Prospective Observational Study of Active Surveillance in Primary Desmoid Fibromatosis.
Chiara ColomboMarco FioreGiovanni GrignaniFrancesco TolomeoAlessandra MerliniElena PalassiniPaola ColliniSilvia StacchiottiPaolo Giovanni CasaliFederica PerroneLuigi MarianiAlessandro GronchiPublished in: Clinical cancer research : an official journal of the American Association for Cancer Research (2022)
In primary DF, AS can be proposed, because disease stabilization and spontaneous regression frequently occur. However, extra care should be taken for patients with tumors of larger size, extremity location, and S45F mutation. See related commentary by Greene and Van Tine, p. 3911.