The SPEC score-A quantifiable CT scoring system for primary ciliary dyskinesia.
Tarika ChowdharyJennifer BrackenLucy MorganAndré SchultzPhilip J RobinsonPublished in: Pediatric pulmonology (2023)
Using PCD-derived data we describe the construct of a PCD-specific score for assessing lung structural damage on CT scans, the SPEC score. A strong correlation between the SPEC score and PFT variables was identified. The SPEC score holds the potential for describing longitudinal changes in CT scans and assessing the efficacy of interventive therapies in patients with PCD.