Perianal/perineal rhabdomyosarcoma: Results of the SIOP MMT 95, Italian RMS 96, and EpSSG RMS 2005 studies.
Timothy N RogersIlaria ZanettiBeatrice CoppadoroHélène MartelliMeriel JenneyVeronique Minard ColinSheila E J Terwisscha van ScheltingaClare SkerrittRaquel Davila FajardoFlorent GuerinAnna KelseyJohannes H M MerksHenry MandevilleGabriela GuillénHeidi GlosliFederica De CortiGianni BisognoPublished in: Pediatric blood & cancer (2022)
About 60% of patients with nonmetastatic PRMS survive; older patients and those with large tumors have the worst outcomes. Biopsy should be the initial procedure, and definitive local therapy individualized. Quality-of-life and functional studies are needed to better understand the consequences of treatment.