Localised Versus Systemic Granulomatosis with Polyangiitis: Data from the French Vasculitis Study Group Registry.
Michele IudiciChristian PagnouxDelphine S CourvoisierPascal CohenAntoine NéelAchille AoubaFrançois LifermannMarc RuivardOlivier AumaîtreBernard BonnotteFrançois MaurierThomas Le GallouEric HachullaAlexandre KarrasChahéra KhouatraNoémie Jourde-ChicheJean-François ViallardClaire Blanchard-DelaunayPascal GodmerAlain Le QuellecThomas QuéméneurClaire de MoreuilAlexis RégentBenjamin TerrierLuc MouthonLoïc GuillevinXavier Puechalnull nullPublished in: Rheumatology (Oxford, England) (2021)
The relapse risks of L-GPA and S-GPA were similar, but relapse patterns differed and L-GPA overall survival rate was higher. About one-quarter of L-GPA patients developed S-GPA over time, but without end-stage organ involvement.