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Anti-Ku antibody-positive systemic sclerosis-polymyositis overlap syndrome in an adolescent.

Rory J LooJames J NoctonMatthew M HarmelinkYvonne E Chiu
Published in: Pediatric dermatology (2020)
Systemic sclerosis-polymyositis overlap syndrome is rare in children. Anti-PM/Scl is the most common autoantibody associated with this syndrome. We present a case of systemic sclerosis-polymyositis overlap syndrome in a child with isolated anti-Ku antibodies, an uncommon antibody associated with this rare syndrome.
Keyphrases
  • systemic sclerosis
  • interstitial lung disease
  • young adults
  • mental health
  • idiopathic pulmonary fibrosis
  • risk assessment
  • polycyclic aromatic hydrocarbons