The 2021 European Alliance of Associations for Rheumatology/American College of Rheumatology Points to Consider for Diagnosis and Management of Autoinflammatory Type I Interferonopathies: CANDLE/PRAAS, SAVI, and AGS.
Kader Cetin GedikLovro LamotMicol RomanoErkan DemirkayaDavid PiskinSofia TorreggianiLaura A AdangThais ArmangueKathe BarchusDevon R CordovaYanick J CrowRussell C DaleKaren L DurrantDespina EleftheriouElisa M FazziMarco GattornoFrancesco GavazziEric P HansonMin Ae Lee-KirschGina A Montealegre SanchezBénédicte NevenSimona OrcesiSeher SenerM Cecilia PoliElliot SchumacherDavide TondutiKatsiaryna UssDaniel AletahaBrian M FeldmanAdeline VanderverPaul A BroganRaphaela Goldbach ManskyPublished in: Arthritis & rheumatology (Hoboken, N.J.) (2022)
These points to consider represent state-of-the-art knowledge to guide diagnostic evaluation, treatment, and management of patients with CANDLE/PRAAS, SAVI, and AGS and aim to standardize and improve care, quality of life, and disease outcomes.