Renal Involvement in Hereditary Transthyretin Amyloidosis: An Italian Single-Centre Experience.
Pietro Manuel FerraroViola D'AmbrosioAndrea Di PaolantonioValeria GuglielminoPaolo CalabresiMario SabatelliMarco LuigettiPublished in: Brain sciences (2021)
Kidney involvement is quite common in patients with ATTRv regardless of the underlying genetic variant. In particular, abnormal UPE appears to be a common feature of the disease.