Overall mortality in combined pulmonary fibrosis and emphysema related to systemic sclerosis.
Alarico ArianiMario SilvaElena BraviSimone ParisiMarta SaraccoFabio De GennaroCristian CaimmiFrancesco GirelliMaria De SantisAlessandro VolpeFederica LumettiVanessa HaxMarkus BredemeierVeronica AlfieriDaniele SantilliFlavio Cesare BodiniGianluca LucchiniFlavio MozzaniValeria SelettiEmanuele BacchiniEugenio ArrigoniDilia GiuggioliRafael ChakrLuca IdolazziGiuseppina BertorelliDavide ImbertiEmanuele MichielettiGiuseppe PaolazziEnrico FusaroAlfredo Antonio ChettaAnd Carlo Alberto ScirèNicola SverzellatiPublished in: RMD open (2019)
CPFE increases the mortality risk in SSc along with a highly impaired lung function. These findings strengthen the importance to take into account emphysema in patients with SSc with ILD.