In vivo characterization of skeletal muscle function in nebulin-deficient mice.
Charlotte GinesteAugustin C OgierIsabelle VarletZaynab HouraniMonique BernardHenk GranzierDavid BendahanJulien GondinPublished in: Muscle & nerve (2020)
Adult nebulin-deficient mice displayed severe muscle atrophy and weakness in vivo related to a low NEB content but an improved fatigue resistance due to a slower contractile phenotype.