Anesthetic management of pediatric patients with Niemann-Pick disease type C for intrathecal 2-hydroxypropyl-β-cyclodextrin injection.
Morgan L UlloaAlexander B FroyshteterLauren N KretDenise P ChangGabriel E SarahRobert J McCarthySteve D BarnesElizabeth M Berry-KravisPublished in: Paediatric anaesthesia (2020)
Our findings suggest that general anesthesia induced via inhalation induction and maintained with volatile anesthetic via mask or supraglottic airway is a safe and effective option for pediatric patients with Niemann-Pick disease type C undergoing serial intrathecal injections of 2-hydroxypropyl-beta-cyclodextrin, supporting this technique as a viable option for anesthetic care in these patients.