Giant right atrium and subvalvular pulmonary stenosis: A case report of an interesting combination.
Viviana MaestriniLucia I BirtoloSara CiminoPaolo SeverinoMassimo ManconeMarco FranconeSanjay M BanypersadFlavia VentrigliaLuigi TritapepeFabio MiraldiFrancesco FedelePublished in: Echocardiography (Mount Kisco, N.Y.) (2019)
A 20-year-old Congolese woman presented with presyncope, dyspnea, and anasarca. Past medical history was unremarkable. Echocardiography revealed a rare combination of giant right atrium (RA), a dilated and hypertrophied right ventricle, subvalvular pulmonary stenosis (subPS), severe tricuspid regurgitation (TR), pericardial effusion and what appeared to be a spontaneously closed ventricular septal defect (VSD). Cardiac Magnetic Resonance and Cardiac Computed Tomography confirmed the findings excluding the presence of intra-cardiac and extra-cardiac shunt and other associated congenital anomalies. The patient underwent subPS resection, right atrioplasty, and tricuspid annuloplasty. Multimodality approach facilitated the detection of the abnormalities and provided clarity when determining the optimal surgical strategy.
Keyphrases
- left ventricular
- mitral valve
- pulmonary hypertension
- computed tomography
- pulmonary artery
- magnetic resonance
- aortic stenosis
- aortic valve
- heart failure
- transcatheter aortic valve replacement
- magnetic resonance imaging
- case report
- inferior vena cava
- coronary artery
- early onset
- catheter ablation
- contrast enhanced
- vena cava
- pulmonary embolism
- coronary artery disease
- interstitial lung disease