Right Ventricle Involvement by Glycogen Storage Cardiomyopathy (PRKAG2): Standard and Advanced Echocardiography Analyses.
Jose Luiz Barros PenaFabricio Junqueira de MeloWander Costa SantosIsabel Cristina Gomes MouraGabriela Pansanato NakashimaNatalia Costa FreitasEduardo Back SternickPublished in: Arquivos brasileiros de cardiologia (2022)
RV involvement in PRKAG2 syndrome is frequent, occurring in different degrees. Echocardiography is a valuable tool in detecting RV myocardial abnormalities in this condition. The use of 2D RV4LS, RVFWLS, and 3DEF offers reliable indicators of RV systolic dysfunction in this rare, challenging cardiomyopathy.