Hemophagocytic lymphohistiocytosis in pregnancy evolving towards fulminant hepatitis.
Camille SimardMarie-Lou TardifPublished in: Obstetric medicine (2021)
Hemophagocytic lymphohistiocytosis is life-threatening and associated with significant morbidity and mortality. Important treatment considerations in pregnancy include maternal health, fetal prematurity and treatment toxicity. Anakinra has been successfully used in pregnancy and provides a promising alternative.