Dietary management and growth outcomes in children with propionic acidemia: A natural history study.
Haneen SaleemaniCsilla EgriGabriella HorvathSylvia Stockler-IpsirogluRajavel ElangoPublished in: JIMD reports (2021)
Despite adequate total protein and energy intakes, all children had persistently low height Z scores. Restricted intact protein consumption together with the abundant use of medical formula could have affected overall growth. To optimize dietary management in patients with PROP, further research is needed to determine the optimal intake of medical formula relative to intact protein.