Endobronchial vasculitis in childhood granulomatosis with polyangiitis.
Matthew D WongLeanne M GauldPublished in: Respirology case reports (2021)
Laryngo-tracheo-bronchial disease in childhood granulomatosis with polyangiitis may acutely present with endobronchial small vessel vasculitis without airway stenosis. Treatment should not be delayed in the presence of haemoptysis as it may indicate acute pulmonary capillaritis which can lead to fatal respiratory failure from diffuse alveolar haemorrhage.
Keyphrases
- respiratory failure
- extracorporeal membrane oxygenation
- mechanical ventilation
- ultrasound guided
- early life
- pulmonary hypertension
- childhood cancer
- liver failure
- acute respiratory distress syndrome
- low grade
- intensive care unit
- young adults
- fine needle aspiration
- combination therapy
- replacement therapy
- smoking cessation