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Cardiovascular manifestations of Erdheim-Chester disease.

Amaninderapal S GhotraKara ThompsonJuan Lopez-MatteiDanish BawaRicardo HernandezJose BanchsNicolas PalaskasCezar IliescuPeter KimSyed Wamique YusufSaamir A Hassan
Published in: Echocardiography (Mount Kisco, N.Y.) (2018)
Erdheim-Chester disease can involve various cardiovascular structures and is frequently diagnosed on an imaging modality. Some patients had asymptomatic involvement, but others presented with ischemic heart disease, heart failure, valvular disease, and conduction system abnormalities. Early recognition of cardiovascular involvement of Erdheim-Chester disease is needed because of high morbidity and mortality.
Keyphrases
  • heart failure
  • high resolution
  • ejection fraction
  • prognostic factors