Clinical features and management of children with primary ciliary dyskinesia in England.

Bruna RubboSunayna BestRobert Anthony HirstAmelia ShoemarkPatricia GogginSiobhan B CarrPhilip ChetcutiClaire HoggPriti KeniaJane S LucasEduardo MoyaManjith NarayananChristopher O'CallaghanMichael WilliamsonWoolf Theodore Walkernull null

Published in: Archives of disease in childhood (2020)

We provide evidence that children with PCD in England have worse lung function than those with CF. Nutritional status should be considered in PCD management, as those with a lower BMI have significantly lower FEV1. Hearing impairment is common but seems to improve with age. Well-designed and powered randomised controlled trials on management of PCD are needed to inform best clinical practice.

Keyphrases

lung function
cystic fibrosis
clinical practice
young adults
chronic obstructive pulmonary disease
air pollution
physical activity