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Cutaneous manifestation of IgG4-related disease mimicking dermatitis artefacta.

Vivek Ashoka MenonElissa TongDana Rose-Marie Louise SlapeTai Anh PhanRenee Cf Chan
Published in: The Australasian journal of dermatology (2019)
Dermatitis artefacta is a self-inflicted cutaneous disease presenting as sharply delineated ulcers, usually in accessible sites such as the head and neck. IgG4-related disease (IgG4-RD) is a recently recognised immune-mediated condition causing a fibroinflammatory process, resulting in the formation of tumefactive lesions in various organs, rarely presenting primarily in the skin. We report a case of cutaneous IgG4-RD clinically presenting as dermatitis artefacta.
Keyphrases
  • atopic dermatitis
  • soft tissue