Login / Signup

A Rare Cause of Recurrent Spontaneous Pneumothorax: Birt-Hogg-Dube Syndrome.

Engin KaramanFurkan UfukMahmut DemirciHüseyin Gökhan Yavaş
Published in: Turkish thoracic journal (2018)
Birt-Hogg-Dube (BHD) syndrome is an unusual disorder characterized by the triad of cutaneous lesions, renal tumors and lung cysts. In cases with BHD syndrome, the frequency of recurrent pneumothorax is increased due to presence of multiple lung cysts. It is important to evaluate the BHD syndrome in differential diagnosis of recurrent pneumothorax especially with multiple lung cysts predominating in the lung base. In these patients, the presence of accompanying kidney and other tumors should be investigated. Herein, we report a case of BHD syndrome presenting with recurrent pneumothorax.
Keyphrases
  • case report
  • end stage renal disease
  • ejection fraction
  • newly diagnosed
  • prognostic factors
  • peritoneal dialysis