Validation of Classification Criteria of Macrophage Activation Syndrome in Japanese Patients With Systemic Juvenile Idiopathic Arthritis.
Masaki ShimizuMao MizutaTakahiro YasumiNaomi IwataYuka OkuraNoriko KinjoHiroaki UmebayashiTomohiro KubotaYasuo NakagishiKenichi NishimuraMasato YashiroJunko YasumuraKazuko YamazakiHiroyuki WakiguchiNami OkamotoMasaaki MoriPublished in: Arthritis care & research (2018)
The classification criteria for MAS complicating systemic JIA had a very high diagnostic performance. However, the diagnostic sensitivity for MAS onset was relatively low. For the early diagnosis of MAS in systemic JIA, the dynamics of laboratory values during the course of MAS should be further investigated.