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Treatment for macrophage activation syndrome associated with systemic juvenile idiopathic arthritis in Japan.

Masaki ShimizuKenichi NishimuraNaomi IwataTakahiro YasumiHiroaki UmebayashiYasuo NakagishiYuka OkuraNami OkamotoNoriko KinjoMao MizutaMasato YashiroJunko YasumuraHiroyuki WakiguchiTomohiro KubotaMariko MouriUtako KanekoMasaaki Mori
Published in: International journal of rheumatic diseases (2023)
The first-line treatment for MAS in Japan is mPSL pulse therapy and/or CyA. DEX-P could be an effective and safe therapeutic option for patients with corticosteroid-resistant MAS.
Keyphrases
  • juvenile idiopathic arthritis
  • blood pressure
  • adipose tissue
  • disease activity
  • case report
  • mesenchymal stem cells
  • rheumatoid arthritis
  • cell therapy