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Paraneoplastic pemphigus: A detailed case series from the Netherlands revealing atypical cases.

Farhat ZaheriHendri H PasJeroen BremerJoost M MeijerMarieke C BollingBarbara HorvathGilles F H Diercks
Published in: Journal of the European Academy of Dermatology and Venereology : JEADV (2022)
Although our findings showed similarities to previous studies and most of the patients met the criteria, there were a few atypical patient cases; highlighting the importance of not strictly adhering to the set criteria when making a diagnosis, as this can lead to a missed or late diagnosis. Thus, it is of crucial importance to combine clinical and elaborate laboratory results to confirm the diagnosis of PNP in suspected patients. Although PNP harbours an unfavourable prognosis in most cases, it might be resolved by timely treatment of the underlying cause.
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