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Inclusion body myositis with early onset: a population-based study.

Ulrika LindgrenCarola Hedberg-OldforsRille PulleritsChristopher LindbergAnders Oldfors
Published in: Journal of neurology (2023)
Early-onset IBM is a severe disease, causing progressive muscle weakness, high muscle mitochondrial DNA mutation load and a reduced cumulative survival in young and middle-aged individuals.
Keyphrases
  • early onset
  • mitochondrial dna
  • middle aged
  • copy number
  • late onset
  • skeletal muscle
  • multiple sclerosis
  • interstitial lung disease
  • myasthenia gravis
  • free survival
  • gene expression