Physiological predictors of survival in patients with sarcoidosis-associated pulmonary hypertension: results from an international registry.
Oksana A ShlobinVasilis KouranosScott D BarnettEsam H AlhamadDaniel A CulverJoseph BarneyFrancis C CordovaEva M CarmonaMary Beth ScholandMarlies WijsenbeekSivagini GaneshElyse E LowerPeter J EngelJohn WortLaura PriceAthol U WellsSteven D NathanRobert P BaughmanPublished in: The European respiratory journal (2020)
Reduced D LCO (<35% pred) and 6MWD (<300 m) at the time of registry enrolment were associated with reduced transplant-free survival in the overall precapillary cohort. Preserved FEV1/FVC ratio was identified as an independent risk factor for worsened outcomes.