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Nutritional Status and Circulating Levels of Fat-Soluble Vitamins in Cystic Fibrosis Patients: A Cohort Study and Evaluation of the Effect of CFTR Modulators.

Michela FrancalanciVito TerlizziCristina FevolaGiulia Di RosaValentina PierattiniElena RoselliPaolo BonomiMaria Chiara CavicchiValeria GaliciAnna Silvia NeriChiara BianchimaniSilvia CampanaDaniela DolceNovella RavenniErica CameraTommaso OrioliGiovanni Taccetti
Published in: Children (Basel, Switzerland) (2023)
Malnutrition is present in a limited number of subjects. The prevalence of subjects with suboptimal 25(OH)D levels is high. ETI showed a beneficial effect on nutritional status and circulating levels of fat-soluble vitamins.
Keyphrases
  • cystic fibrosis
  • adipose tissue
  • end stage renal disease
  • ejection fraction
  • newly diagnosed
  • small molecule
  • risk factors
  • lung function
  • chronic obstructive pulmonary disease