Brunhilde Wirth

Scopus Author ID ORCID

Publication Activity (10 Years)

Years Active: 2018-2024
Publications (10 Years): 37

Top Topics

Endoplasmic Reticulum

Highly Efficient

Top Venues

International journal of molecular sciences

Nature communications

Science advances

This page only lists publications with an associated author ORCID identifier.

Publications

Wenchao Zhong, Janine Neugebauer, Janak L Pathak, Xingyang Li, Gerard Pals, M Carola Zillikens, Elisabeth M W Eekhoff, Nathalie Bravenboer, Qingbin Zhang, Matthias Hammerschmidt, Brunhilde Wirth, Dimitra Micha
Functional Insights in PLS3-Mediated Osteogenic Regulation. Cells 13 (17) (2024)
Marta Zaninello, Tim Schlegel, Hendrik Nolte, Mujeeb Pirzada, Elisa Savino, Esther Barth, Ines Klein, Hauke Wüstenberg, Tesmin Uddin, Lisa Wolff, Brunhilde Wirth, Helmar C Lehmann, Jean-Michel Cioni, Thomas Langer, Elena I Rugarli
CLUH maintains functional mitochondria and translation in motoneuronal axons and prevents peripheral neuropathy. Science advances 10 (22) (2024)
Ilka Maus, Maren Dreiner, Sebastian Zetzsche, Fabian Metzen, Bryony C Ross, Daniela Mählich, Manuel Koch, Anja Niehoff, Brunhilde Wirth
Osteoclast-specific Plastin 3 knockout in mice fail to develop osteoporosis despite dramatic increased osteoclast resorption activity. JBMR plus 8 (1) (2024)
Ilka Maus, Maren Dreiner, Sebastian Zetzsche, Fabian Metzen, Bryony C Ross, Daniela Mählich, Manuel Koch, Anja Niehoff, Brunhilde Wirth
Osteoclast-specific Plastin 3 knockout in mice fail to develop osteoporosis despite dramatic increased osteoclast resorption activity. JBMR plus 8 (1) (2024)
Ilka Maus, Maren Dreiner, Sebastian Zetzsche, Fabian Metzen, Bryony C Ross, Daniela Mählich, Manuel Koch, Anja Niehoff, Brunhilde Wirth
Osteoclast-specific Plastin 3 knockout in mice fail to develop osteoporosis despite dramatic increased osteoclast resorption activity. JBMR plus 8 (1) (2024)
Rachel James, Kiterie M E Faller, Ewout Joan Nicolaas Groen, Brunhilde Wirth, Thomas Henry Gillingwater
Altered mitochondrial function in fibroblast cell lines derived from disease carriers of spinal muscular atrophy. Communications medicine 4 (1) (2024)
Marta Zaninello, Tim Schlegel, Hendrik Nolte, Mujeeb Pirzada, Elisa Savino, Esther Barth, Ines Klein, Hauke Wüstenberg, Tesmin Uddin, Lisa Wolff, Brunhilde Wirth, Helmar C Lehmann, Jean-Michel Cioni, Thomas Langer, Elena I Rugarli
CLUH maintains functional mitochondria and translation in motoneuronal axons and prevents peripheral neuropathy. Science advances 10 (22) (2024)
Marta Zaninello, Tim Schlegel, Hendrik Nolte, Mujeeb Pirzada, Elisa Savino, Esther Barth, Ines Klein, Hauke Wüstenberg, Tesmin Uddin, Lisa Wolff, Brunhilde Wirth, Helmar C Lehmann, Jean-Michel Cioni, Thomas Langer, Elena I Rugarli
CLUH maintains functional mitochondria and translation in motoneuronal axons and prevents peripheral neuropathy. Science advances 10 (22) (2024)
Rachel James, Kiterie M E Faller, Ewout Joan Nicolaas Groen, Brunhilde Wirth, Thomas Henry Gillingwater
Altered mitochondrial function in fibroblast cell lines derived from disease carriers of spinal muscular atrophy. Communications medicine 4 (1) (2024)
Ilka Maus, Maren Dreiner, Sebastian Zetzsche, Fabian Metzen, Bryony C Ross, Daniela Mählich, Manuel Koch, Anja Niehoff, Brunhilde Wirth
Osteoclast-specific Plastin 3 knockout in mice fail to develop osteoporosis despite dramatic increased osteoclast resorption activity. JBMR plus 8 (1) (2024)
Rachel James, Kiterie M E Faller, Ewout Joan Nicolaas Groen, Brunhilde Wirth, Thomas Henry Gillingwater
Altered mitochondrial function in fibroblast cell lines derived from disease carriers of spinal muscular atrophy. Communications medicine 4 (1) (2024)
Anixa Muiños-Bühl, Roman Rombo, Karen K Ling, Eleonora Zilio, Frank Rigo, C Frank Bennett, Brunhilde Wirth
Long-Term SMN - and Ncald -ASO Combinatorial Therapy in SMA Mice and NCALD -ASO Treatment in hiPSC-Derived Motor Neurons Show Protective Effects. International journal of molecular sciences 24 (4) (2023)
Biljana Ermanoska, Bob Asselbergh, Laura Morant, Maria-Luise Petrovic-Erfurth, Seyyedmohsen Hosseinibarkooie, Ricardo Leitão-Gonçalves, Leonardo Almeida-Souza, Sven Bervoets, Litao Sun, LaTasha Lee, Derek Atkinson, Akram Khanghahi, Ivaylo Tournev, Patrick Callaerts, Patrik Verstreken, Xiang-Lei Yang, Brunhilde Wirth, Avital Adah Rodal, Vincent Timmerman, Bruce L Goode, Tanja A Godenschwege, Albena Jordanova
Tyrosyl-tRNA synthetase has a noncanonical function in actin bundling. Nature communications 14 (1) (2023)
Nur Cengiz Winter, Mert Karakaya, Peter Mosen, Isabell Brusius, Banu Anlar, Goknur Haliloglu, Dominic Winter, Brunhilde Wirth
Proteomic Investigation of Differential Interactomes of Glypican 1 and a Putative Disease-Modifying Variant of Ataxia. Journal of proteome research (2023)
Biljana Ermanoska, Bob Asselbergh, Laura Morant, Maria-Luise Petrovic-Erfurth, Seyyedmohsen Hosseinibarkooie, Ricardo Leitão-Gonçalves, Leonardo Almeida-Souza, Sven Bervoets, Litao Sun, LaTasha Lee, Derek Atkinson, Akram Khanghahi, Ivaylo Tournev, Patrick Callaerts, Patrik Verstreken, Xiang-Lei Yang, Brunhilde Wirth, Avital Adah Rodal, Vincent Timmerman, Bruce L Goode, Tanja A Godenschwege, Albena Jordanova
Tyrosyl-tRNA synthetase has a noncanonical function in actin bundling. Nature communications 14 (1) (2023)
Anixa Muiños-Bühl, Roman Rombo, Karen K Ling, Eleonora Zilio, Frank Rigo, C Frank Bennett, Brunhilde Wirth
Long-Term SMN - and Ncald -ASO Combinatorial Therapy in SMA Mice and NCALD -ASO Treatment in hiPSC-Derived Motor Neurons Show Protective Effects. International journal of molecular sciences 24 (4) (2023)
Anixa Muiños-Bühl, Roman Rombo, Karen K Ling, Eleonora Zilio, Frank Rigo, C Frank Bennett, Brunhilde Wirth
Long-Term SMN - and Ncald -ASO Combinatorial Therapy in SMA Mice and NCALD -ASO Treatment in hiPSC-Derived Motor Neurons Show Protective Effects. International journal of molecular sciences 24 (4) (2023)
Anixa Muiños-Bühl, Roman Rombo, Karen K Ling, Eleonora Zilio, Frank Rigo, C Frank Bennett, Brunhilde Wirth
Long-Term SMN - and Ncald -ASO Combinatorial Therapy in SMA Mice and NCALD -ASO Treatment in hiPSC-Derived Motor Neurons Show Protective Effects. International journal of molecular sciences 24 (4) (2023)
Anixa Muiños-Bühl, Roman Rombo, Karen K Ling, Eleonora Zilio, Frank Rigo, C Frank Bennett, Brunhilde Wirth
Long-Term SMN - and Ncald -ASO Combinatorial Therapy in SMA Mice and NCALD -ASO Treatment in hiPSC-Derived Motor Neurons Show Protective Effects. International journal of molecular sciences 24 (4) (2023)
Biljana Ermanoska, Bob Asselbergh, Laura Morant, Maria-Luise Petrovic-Erfurth, Seyyedmohsen Hosseinibarkooie, Ricardo Leitão-Gonçalves, Leonardo Almeida-Souza, Sven Bervoets, Litao Sun, LaTasha Lee, Derek Atkinson, Akram Khanghahi, Ivaylo Tournev, Patrick Callaerts, Patrik Verstreken, Xiang-Lei Yang, Brunhilde Wirth, Avital Adah Rodal, Vincent Timmerman, Bruce L Goode, Tanja A Godenschwege, Albena Jordanova
Tyrosyl-tRNA synthetase has a noncanonical function in actin bundling. Nature communications 14 (1) (2023)
Biljana Ermanoska, Bob Asselbergh, Laura Morant, Maria-Luise Petrovic-Erfurth, Seyyedmohsen Hosseinibarkooie, Ricardo Leitão-Gonçalves, Leonardo Almeida-Souza, Sven Bervoets, Litao Sun, LaTasha Lee, Derek Atkinson, Akram Khanghahi, Ivaylo Tournev, Patrick Callaerts, Patrik Verstreken, Xiang-Lei Yang, Brunhilde Wirth, Avital Adah Rodal, Vincent Timmerman, Bruce L Goode, Tanja A Godenschwege, Albena Jordanova
Tyrosyl-tRNA synthetase has a noncanonical function in actin bundling. Nature communications 14 (1) (2023)
Eleonora Zilio, Valentina Piano, Brunhilde Wirth
Mitochondrial Dysfunction in Spinal Muscular Atrophy. International journal of molecular sciences 23 (18) (2022)
Sofia Vrettou, Brunhilde Wirth
S-Glutathionylation and S-Nitrosylation in Mitochondria: Focus on Homeostasis and Neurodegenerative Diseases. International journal of molecular sciences 23 (24) (2022)
Sofia Vrettou, Brunhilde Wirth
S-Glutathionylation and S-Nitrosylation in Mitochondria: Focus on Homeostasis and Neurodegenerative Diseases. International journal of molecular sciences 23 (24) (2022)
Sofia Vrettou, Brunhilde Wirth
S-Glutathionylation and S-Nitrosylation in Mitochondria: Focus on Homeostasis and Neurodegenerative Diseases. International journal of molecular sciences 23 (24) (2022)
Sofia Vrettou, Brunhilde Wirth
S-Glutathionylation and S-Nitrosylation in Mitochondria: Focus on Homeostasis and Neurodegenerative Diseases. International journal of molecular sciences 23 (24) (2022)
Andrea Delle Vedove, Janani Natarajan, Ginevra Zanni, Matthias Eckenweiler, Anixa Muiños-Bühl, Markus Storbeck, Jordina Guillén Boixet, Sabina Barresi, Simone Pizzi, Irmgard Hölker, Friederike Körber, Titus M Franzmann, Enrico S Bertini, Janbernd Kirschner, Simon Alberti, Marco Tartaglia, Brunhilde Wirth
CAPRIN1 P512L causes aberrant protein aggregation and associates with early-onset ataxia. Cellular and molecular life sciences : CMLS 79 (10) (2022)
Melina Overhoff, Frederik Tellkamp, Simon Hess, Marianna Tolve, Janine Tutas, Marcel Faerfers, Lotte Ickert, Milad Mohammadi, Elodie De Bruyckere, Emmanouela Kallergi, Andrea Delle Vedove, Vassiliki Nikoletopoulou, Brunhilde Wirth, Joerg Isensee, Tim Hucho, Dmytro Puchkov, Dirk Isbrandt, Marcus Krueger, Peter Kloppenburg, Natalia L Kononenko
Autophagy regulates neuronal excitability by controlling cAMP/protein kinase A signaling at the synapse. The EMBO journal 41 (22) (2022)
Lisa Pavinato, Andrea Delle Vedove, Diana Carli, Marta Ferrero, Silvia Carestiato, Jennifer L Howe, Emanuele Agolini, Domenico A Coviello, Ingrid van de Laar, Ping Yee Billie Au, Eleonora Di Gregorio, Alessandra Fabbiani, Susanna Croci, Maria Antonietta Mencarelli, Lucia P Bruno, Alessandra Renieri, Danai Veltra, Christalena Sofocleous, Laurence Faivre, Benoit Mazel, Hana Safraou, Anne Sophie Denommé-Pichon, Marjon A van Slegtenhorst, Noor Giesbertz, Richard H van Jaarsveld, Anna Childers, R Curtis Rogers, Antonio Novelli, Silvia De Rubeis, Joseph D Buxbaum, Stephen W Scherer, Giovanni Battista Ferrero, Brunhilde Wirth, Alfredo Brusco
CAPRIN1 haploinsufficiency causes a neurodevelopmental disorder with language impairment, ADHD and ASD. Brain : a journal of neurology (2022)
Lu Chen, Caitlin M Roake, Paolo Maccallini, Francesca Bavasso, Roozbeh Dehghannasiri, Pamela Santonicola, Natalia Mendoza-Ferreira, Livia Scatolini, Ludovico Rizzuti, Alessandro Esposito, Ivan Gallotta, Sofia Francia, Stefano Cacchione, Alessandra Galati, Valeria Palumbo, Marie A Kobin, Gian Gaetano Tartaglia, Alessio Colantoni, Gabriele Proietti, Yunming Wu, Matthias Hammerschmidt, Cristiano De Pittà, Gabriele Sales, Julia Salzman, Livio Pellizzoni, Brunhilde Wirth, Elia Di Schiavi, Maurizio Gatti, Steven E Artandi, Grazia Daniela Raffa
TGS1 impacts snRNA 3'-end processing, ameliorates survival motor neuron-dependent neurological phenotypes in vivo and prevents neurodegeneration. Nucleic acids research (2022)
Natalie Keller, Cem Paketci, Janine Altmueller, Nico Fuhrmann, Gilbert Wunderlich, Bertold Schrank, Olcay Unver, Sanem Yilmaz, Reza Boostani, Ehsan Ghayoor Karimiani, Susanne Motameny, Holger Thiele, Peter Nürnberg, Reza Maroofian, Uluc Yis, Brunhilde Wirth, Mert Karakaya
Genomic variants causing mitochondrial dysfunction are common in hereditary lower motor neuron disease. Human mutation 42 (4) (2021)
Lisa Wolff, Eike A Strathmann, Ilka Müller, Daniela Mählich, Charlotte Veltman, Anja Niehoff, Brunhilde Wirth
Plastin 3 in health and disease: a matter of balance. Cellular and molecular life sciences : CMLS 78 (13) (2021)
Daniela Mählich, Anne Glasmacher, Ilka Müller, Johannes Oppermann, David Grevenstein, Peer Eysel, Juliane Heilig, Brunhilde Wirth, Frank Zaucke, Anja Niehoff
Expression and Localization of Thrombospondins, Plastin 3, and STIM1 in Different Cartilage Compartments of the Osteoarthritic Varus Knee. International journal of molecular sciences 22 (6) (2021)
Maximilian Paul Thelen, Brunhilde Wirth, Min Jeong Kye
Mitochondrial defects in the respiratory complex I contribute to impaired translational initiation via ROS and energy homeostasis in SMA motor neurons. Acta neuropathologica communications 8 (1) (2020)
Mert Karakaya, Cem Paketci, Janine Altmueller, Holger Thiele, Irmgard Hoelker, Uluc Yis, Brunhilde Wirth
Biallelic variant in AGTPBP1 causes infantile lower motor neuron degeneration and cerebellar atrophy. American journal of medical genetics. Part A 179 (8) (2019)
Mert Karakaya, Markus Storbeck, Eike A Strathmann, Andrea Delle Vedove, Irmgard Hölker, Janine Altmueller, Leyla Naghiyeva, Lea Schmitz-Steinkrüger, Katharina Vezyroglou, Susanne Motameny, Salem Alawbathani, Holger Thiele, Ayse Ipek Polat, Derya Okur, Reza Boostani, Ehsan Ghayoor Karimiani, Gilbert Wunderlich, Didem Ardicli, Haluk Topaloglu, Janbernd Kirschner, Bertold Schrank, Reza Maroofian, Olafur Magnusson, Uluc Yis, Peter Nürnberg, Raoul Heller, Brunhilde Wirth
Targeted sequencing with expanded gene profile enables high diagnostic yield in non-5q-spinal muscular atrophies. Human mutation 39 (9) (2018)
Eike A Strathmann, Miriam Peters, Seyyedmohsen Hosseinibarkooie, Frank W Rigo, C Frank Bennett, Phillip G Zaworski, Karen S Chen, Michael Nothnagel, Brunhilde Wirth
Evaluation of potential effects of Plastin 3 overexpression and low-dose SMN-antisense oligonucleotides on putative biomarkers in spinal muscular atrophy mice. PloS one 13 (9) (2018)