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Kaposiform Hemangioendothelioma Presenting as Hydrops Fetalis.

Elena Sobrino-FernándezMinia Campos-DominguezRebeca Gregorio-HernándezJorge Huerta-AragonésCristina Beléndez-BielerÁngel Lancharro-ZapataMaría Luisa Franco-FernándezBelén Bernardo-AtienzaManuel Sánchez-Luna
Published in: Pediatric dermatology (2017)
We describe the case of a 33-week preterm infant who developed nonimmune hydrops fetalis secondary to a kaposiform hemangioendothelioma (KHE). The tumor was successfully treated with vincristine, prednisone, ticlopidine, and aspirin. KHE can be an unusual cause of hydrops fetalis; in such cases, diagnosis can be challenging since generalized edema can obscure KHE.
Keyphrases
  • low dose
  • preterm birth
  • cardiovascular events
  • low birth weight
  • clinical trial
  • randomized controlled trial
  • cardiovascular disease
  • coronary artery disease
  • preterm infants
  • double blind