Familial Gigantiform Cementoma with Calcium Steal Phenomenon and Social Stigma: A Case Report with Review of Literature.
Subhash C YadavNeha MittalMunita BalSajid QureshiPublished in: Journal of maxillofacial and oral surgery (2021)
Cemento-ossifying fibromas are benign fibro-osseous lesions characterized by deposition of cementum and fibrous tissue. Familial gigantiform cementoma (FGC) is an exceeding rare and distinct subtype of cemento-osseous-fibrous lesion. We hereby present a case of FGC in a young boy who was left to die due to the social stigma caused by the massive bony growth in the upper and lower jaw. The patient was somehow rescued by a non-governmental organization and underwent his surgical management at our hospital. On family screening, the mother also had similar smaller asymptomatic lesions in the jaw, but she refused further investigations and treatment. FGC is frequently associated with "calcium-steal phenomenon," which was also seen in our patient. Family screening is therefore necessary to identify asymptomatic patients in the family and follow them up with radiology and whole body dual-energy absorptiometry scans.
Keyphrases
- dual energy
- computed tomography
- mental health
- healthcare
- case report
- end stage renal disease
- mental illness
- image quality
- hiv aids
- newly diagnosed
- early onset
- prognostic factors
- contrast enhanced
- social support
- magnetic resonance imaging
- bone mineral density
- artificial intelligence
- peritoneal dialysis
- depressive symptoms
- emergency department
- machine learning
- human immunodeficiency virus
- hepatitis c virus
- magnetic resonance
- patient reported