Ultra-rare sarcomas: A consensus paper from the Connective Tissue Oncology Society community of experts on the incidence threshold and the list of entities.
Silvia StacchiottiAnna Maria FrezzaJean Yves BlayElizabeth H BaldiniSylvie BonvalotJudith V M G BovéeDario CallegaroPaolo G CasaliRuRu Chun-Ju ChiangGeorge D DemetriElisabeth G DemiccoJayesh DesaiMikael ErikssonHans GelderblomSuzanne GeorgeMrinal M GounderAlessandro GronchiAbha A GuptaRick L M HaasAndrea Hayes-JardonPeter HohenbergerKevin B JonesRobin L JonesBernd KasperAkira KawaiDavid G KirschEugene S KleinermanAxel Le CesneJiwon LimMaría Dolores Chirlaque LópezRoberta MaestroRafael Marcos-GrageraJavier Martin BrotoTomohiro MatsudaOlivier MirShreyaskumar R PatelChandrajit P RautAlbiruni R A RazakDamon R ReedPiotr RutkowskiRoberta G SanfilippoMarta SbaragliaInga-Marie SchaeferDirk C StraussKirsten Sundby HallWilliam D TapDavid M ThomasWinette T A van der GraafWinan J van HoudtOtto VisserMargaret von MehrenAndrew J WagnerBreelyn A WilkyYoung Joo WonChristopher D M FletcherAngelo P Dei TosAnnalisa TramaPublished in: Cancer (2021)
Altogether, the incidence of ultra-rare sarcomas accounts for roughly 20% of all soft tissue and bone sarcomas. This confirms that the challenges inherent in ultra-rare sarcomas affect large numbers of patients.