Peak oxygen uptake (VO2peak) across childhood, adolescence and young adulthood in Barth syndrome: Data from cross-sectional and longitudinal studies.
William Todd CadeKathryn L BohnertDominic N ReedsLinda R PetersonAdam J BittelAdil BashirBarry J ByrneCarolyn L TaylorPublished in: PloS one (2018)
In conclusion, VO2peak relative to body weight and fat-free mass demonstrates short- and long-term stability from childhood to young adulthood in BTHS with some variability among individuals.