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Current perspectives of sudden cardiac death management in hypertrophic cardiomyopathy.

Lutong PuJialin LiWeitang QiJinquan ZhangHongyu ChenZihuan TangYuchi HanJie WangYucheng Chen
Published in: Heart failure reviews (2023)
Hypertrophic cardiomyopathy (HCM) is an autosomal dominant disorder characterized by left ventricular hypertrophy. Sudden cardiac death (SCD) is a rare but the most catastrophic complication in patients with HCM. Implantable cardioverter-defibrillators (ICDs) are widely recognized as effective preventive measures for SCD. Individualized risk stratification and early intervention in HCM can significantly improve patient prognosis. In this study, we review the latest findings regarding pathogenesis, risk stratification, and prevention of SCD in HCM patients, highlighting the clinic practice of cardiovascular magnetic resonance imaging for SCD management.
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