Lipoprotein Lipase Deficiency.

Shwetha KuthirolyDhanya YesodharanNatasha RadhakrishnanAparna GanapathyAshraf U MannanMichael M HoffmannSheela Nampoothiri

Published in: Indian journal of pediatrics (2020)

Lipemic serum, chylothorax and recurrent pancreatitis in children should raise the suspicion of Lipoprotein Lipase deficiency. Early diagnosis and prompt initiation of a stringent fat-restricted diet are the keys to success for the management of LPL deficiency and prevention of pancreatitis.

Keyphrases

replacement therapy
adipose tissue
weight loss
low density lipoprotein
fatty acid