Cough Effectiveness and Pulmonary Hygiene Practices in Patients with Pompe Disease.

Teresa PittsRachel BordelonAlyssa HuffBarry J ByrneBarbara K Smith

Published in: Lung (2018)

Cough weakness was detected in the majority of patients with Pompe disease and was influenced by both inspiratory and expiratory muscle function. Patients at risk for problems or with ineffective PCF should be urged to complete routine pulmonary hygiene.

Keyphrases

late onset
pulmonary hypertension
replacement therapy
end stage renal disease
ejection fraction
randomized controlled trial
newly diagnosed
mental health
healthcare
systematic review
primary care
skeletal muscle
patient reported outcomes
intensive care unit
patient reported