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Endocrinopathies in Aicardi Goutières syndrome-A descriptive case series.

Christopher WorthTracy A BriggsRaja PadidelaEleanor BalmerMars Skae
Published in: Clinical case reports (2020)
Hypothyroidism and diabetes insipidus present in children with Aicardi Goutières Syndrome (AGS) often years after disease onset and frequently resolve spontaneously. Screening and regular reassessment for both conditions are recommended in all children with AGS.
Keyphrases
  • young adults
  • type diabetes
  • cardiovascular disease
  • case report
  • cross sectional
  • adipose tissue
  • glycemic control
  • insulin resistance
  • skeletal muscle