Anthropometric, Body Composition, and Nutritional Indicators with and without Nutritional Intervention during Nitisinone Therapy in Alkaptonuria.
L R RanganathMilad KhedrAnna M MilanAndrew S DavisonA T HughesBrendan P NormanH BygottE LuangrathS JuddC SoulsbyB OlssonR ImrichPublished in: Nutrients (2024)
Ongoing dietetic intervention prevented loss of lean body mass despite protein restriction and moderated serum tyrosine increase, leading to less prevalent corneal keratopathy. Protein restriction risks fat mass gain.