Individuals with 21 trisomy or Down syndrome (DS) are known to have an increased risk of acute leukemia, while they rarely develop solid or central nervous system (CNS) tumors. Atypical teratoid rhabdoid tumor (ATRT) is a highly aggressive CNS-WHO grade 4 neoplasm, which has never been reported in association with Down syndrome. We present a case study of a 14-year-old female with Down syndrome, diagnosed with intradural-extramedullary spinal ATRT. The chief complaints included bilateral lower limb weakness, constipation, and urinary incontinence for 2 weeks. Surgery was scheduled, and a biopsy was taken. The histopathology, immunohistochemistry, and molecular analysis confirmed the diagnosis of the ATRT-MYC/group 2B subgroup. This report highlights the challenges of managing a patient with complex medical conditions. Moreover, it adds to the existing literature on CNS tumors in patients with Down syndrome.
Keyphrases
- lower limb
- urinary incontinence
- blood brain barrier
- spinal cord
- minimally invasive
- case report
- healthcare
- systematic review
- mental health
- coronary artery bypass
- low grade
- randomized controlled trial
- coronary artery disease
- cerebrospinal fluid
- atrial fibrillation
- surgical site infection
- acute coronary syndrome
- phase iii
- percutaneous coronary intervention