Clinical phenotypes and outcomes of precapillary pulmonary hypertension of sickle cell disease.
Laurent SavaleAnoosha HabibiFrançois LionnetBernard MaitreVincent CottinXavier JaisAri ChaouatElise Artaud-MacariMatthieu CanuetGrégoire PrevotChristelle Chantalat-AugerI David MontaniOlivier SitbonFréderic GalacterosGérald SimonneauFlorence ParentPablo BartolucciMarc HumbertPublished in: The European respiratory journal (2019)
Patients with precapillary PH related to SCD have a poor prognosis. Thrombotic lesions appear as a major component of PH related to SCD, more frequently in SC patients.