Sub-acute neonatal hemochromatosis in an infant with hypoplastic left heart syndrome on ventricular assist device awaiting transplantation.
Hanna J TadrosDipankar GuptaMegan ChildressGenie BeasleyAshlie E RubrechtArchana ShenoyJoseph PhilipMark S BleiweisDesiree S MachadoPublished in: Pediatric transplantation (2019)
Single-ventricle pediatric patients, amongst other children waiting for OHT, are a vulnerable population, especially if candidacy is established before any palliation. NH is a rare disease with poor prognosis in the post-natal period. We present a case of sub-acute NH diagnosed in an infant with HLHS who was listed for OHT while bridged with a pulsatile paracorporeal VAD, with an emphasis on the evolution of the condition throughout the patient's clinical course and the ultimate decision for compassionate deactivation of VAD.
Keyphrases
- poor prognosis
- liver failure
- long non coding rna
- respiratory failure
- heart failure
- case report
- room temperature
- drug induced
- aortic dissection
- young adults
- left ventricular
- mitral valve
- pulmonary hypertension
- atrial fibrillation
- coronary artery
- cell therapy
- congenital heart disease
- decision making
- pulmonary arterial hypertension
- bone marrow
- mechanical ventilation