Acute petrified myocardium associated with meningococcal sepsis in childhood-onset systemic lupus erythematous: a fatal case.
Ana Carolina Etrusco Zaroni SantosMichele LuglioArtur Figueiredo DelgadoConstance Dell Santo Vieira SchuwartzHeloisa Helena de Sousa MarquesClarissa Carvalho de Miranda ValõesMaria Andreina Cabrera DominguezWerther Brunow de B CarvalhoClovis Artur Almeida da SilvaAmaro Nunes DuartePublished in: Revista do Instituto de Medicina Tropical de Sao Paulo (2019)
Acute petrified myocardium associated with septic shock, diagnosed by autopsy has rarely been described. A 15-year-old adolescent male was diagnosed with childhood-onset systemic lupus erythematosus. One year later, he was hospitalized with fever, myalgia, headache, arthritis, vomiting, dyspnea and was diagnosed with sepsis secondary to bronchopneumonia and meningitis. Blood culture identified Neisseria meningitidis serogroup Y. Despite antibiotics and intensive therapeutic measures, he died after 29 days of hospitalization. The autopsy revealed necrotic cardiomyocytes with dystrophic calcification and interstitial fibrosis.
Keyphrases
- septic shock
- systemic lupus erythematosus
- liver failure
- respiratory failure
- disease activity
- drug induced
- aortic dissection
- childhood cancer
- rheumatoid arthritis
- young adults
- acute kidney injury
- mental health
- intensive care unit
- early life
- chronic kidney disease
- hepatitis b virus
- extracorporeal membrane oxygenation
- cerebrospinal fluid
- mechanical ventilation
- abdominal pain
- advanced cancer