Nationwide lung function monitoring from infancy in newborn-screened children with cystic fibrosis.
Rikke M SandvikMarika N SchmidtChristian M VoldbyFrederik F BuchvaldHanne V OlesenJørgen OlsenMaja V KraghSune L M RubakTacjana PresslerPaul D RobinsonPer M GustafssonMarianne SkovKim G NielsenPublished in: ERJ open research (2023)
isolation "ever" was associated with an accelerated deterioration in lung function, while lumacaftor/ivacaftor therapy significantly improved and stabilised the trajectory.