Diagnostic pathways to wild-type transthyretin amyloid cardiomyopathy: a multicentre network study.
Giacomo TiniPaolo MilaniMattia ZampieriAngelo G CaponettiFrancesca FabrisAndrea FoliAlessia ArgiròCarlotta MazzoniChristian GagliardiSimone LonghiGiulia SaturiGiuseppe VergaroAlberto AimoDomitilla RussoGuerino G VarràMatteo SerenelliGioele FabbriLaura De MichieliGiuseppe PalmieroGiuseppe CilibertiSamuela CarigiEugenio SessaregoGiulia E MandoliGiulia Ricci LucchiValeria RellaEnrico MontiElisa GardiniMichela BartolottiLia CrottiElisa MerliRoberta MussinelliPier Filippo VianelloMatteo CameliFrancesca MarzoFederico GuerraGiuseppe LimongelliAlberto CiprianiStefano PerliniLaura ObiciFederico PerfettoCamillo AutoreItalo PortoClaudio RapezziGianfranco SinagraMarco MerloBeatrice MusumeciMichele EmdinElena BiaginiFrancesco CappelliGiovanni PalladiniMarco CanepaPublished in: European journal of heart failure (2023)
Half of contemporary ATTRwt-CA diagnoses occur in a HF setting. These patients had worse clinical profile and outcome than those diagnosed either due to suspected HCM or incidentally, although prognosis remained primarily related to age, NYHA functional class and comorbidities rather than the diagnostic pathway itself.